Superior Semicircular Canal Dehiscence
National Organization for Rare Disorders, Inc.
It is possible that the main title of the report Superior Semicircular Canal Dehiscence is not the name you expected.
Superior semicircular canal dehiscence (SSCD) has been defined as the absence of bone overlying the superior semicircular canal facing toward the dura of the middle cranial fossa. SSCD has been implicated as the cause of a variety of inner ear symptoms including Tullio's phenomenon, pressure induced vertigo, aural fullness, autophony, conductive hearing loss, and fluctuating or progressive sensorineural hearing loss. Additionally, SSCD has also been reported to be asymptomatic. In the past, many patients with SSCD had been misdiagnosed as having otosclerosis, patulous eustachian tubes, middle ear perilymphatic fistulas, or Ménière's disease. Identification of this entity requires a high degree of suspicion, appropriate findings on physical exam, lab testing, and confirmation on high-resolution CT scan. Surgical repair of the SSCD or occlusion of the superior canal has been reported with a high degree of symptom resolution.
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Vestibular Disorders Association (VEDA)
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Last Updated: 3/7/2016
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